PAEDIATRICS: PRACTICE 11

                             SINGLE BEST OPTION SERIES
               INSTRUCTION: SELECT THE SINGLE BEST OPTION.
  

1.        The following are usual characteristics of birth asphyxia livida except:
   a.       Cyanosed skin
   b.      Bradycardia
   c.       Hypotonia
   d.      Reactive pupils
   e.      Presence of respiratory effort.
   2.       Features of congenital syphilis include the following except:
   a.       Rhagades
   b.      Maxillary hyperplasia
   c.       Mulberry molars
   d.      Clutton joints
   e.      Hutchinson’s incisors
   3.       Which of the following is incorrect about megaencephaly?
   a.       It occurs in patients with tuberous sclerosis
   b.      It may naturally occur in children from large-head families
   c.       The commonest cause in infants is hydrocephalus
   d.      All persons with macrocephaly will have megaencephaly
   e.      Measurement of head circumference aids clinical detection
   4.       Which of the following is incorrect about Alexander’s disease?
   a.       It is inherited in an autosomal recessive manner
   b.      Eosinophilic deposits known as Rosenthal fibres is seen in white of the brain of afftected patients
   c.       Patients slowly loose body function and eventually the ability to walk ensues.
   d.      They may present with macrocephaly/megaencephaly.
   e.      It is a cause of developmental delay, spasticity and seizures in younger patients
   5.       Which of the following is incorrect about cerebral neoplasms:
   a.       Cerebral tumours are relatively uncommon in infants and children
   b.      The four main groups of primary tumours in childhood are cerebellar glioma, pontine glioma, medulloblastoma and choroid plexus papillomas
   c.       Secondary neuroblastomas occur mainly in adults
   d.      Posterior fossa tumours are more common in children than in adults
   e.      Astrocytoma and oligodendroglioma are well differentiated slow-growing gliomas
   6.       The following are features of Arnold Chiari malformations except:
   a.       Cerebellar hyperplasia
   b.      Downward displacement of the brainstem
   c.       Occipital encephalocoele
   d.      Thoraco-lumbar myelomeningocoele in type 2 Chiari malformation
   e.      Flat occiput
   7.       The following are found in neurofibromatosis type 2 except:
   a.       Bilateral acoustic neuroma
   b.      Spinal bilateral neurofibromas
   c.       Spinal meningiomas
   d.      Schwannomas
   e.      None of the above
   8.       The following are causes of macrocephaly except:
   a.       Hydrocephalus
   b.      Lipidoses
   c.       Spongy degeneration of the white matter
   d.      Familial
   e.      None of the above
   9.       Which of the following is incorrect about congenital aqueductal stenosis?
   a.       Hydrocephalus involving the fourth ventricle of the brain
   b.      Usually presents in infancy or childhood
   c.       Neurofibromatosis and Chiari type 2 malformation are recognized associations
   d.      There is obstruction of the Aqueduct of Sylvius
   e.      None of the above
   10.   The following are phakomatoses except:
   a.       Tuberous sclerosis
   b.      Multiple sclerosis
   c.       Sturge-Weber disease
   d.      Neurofibromatosis
   e.      Von Hippel-Lindau disease
   
   
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