PAEDIATRICS: PRACTICE 13

SINGLE BEST OPTION SERIES

         INSTRUCTION: SELECT THE SINGLE BEST OPTION

1.       The following are consistent with neurofibromatosis type 1 except:
   a.       It is an autosomal dorminant disorder resulting from defect in chromosome 22
   b.      “Bare orbit” causing unilateral exophthalmos may occur
   c.       Spinal scoliosis or kyphoscoliosis may be present
   d.      Optic nerve glioma, cerebral and brainstem astrocytoma are recognized features
   e.      Generalized or focal cerebral atrophy may also be seen and associated with mental retardation
   2.       The following are features of  Dandy-Walker syndrome except:
   a.       Obstruction to the foramina of Magendie and Luschka
   b.      Cystic constriction of the fourth ventricle
   c.       Macrocephaly
   d.      Hypoplastic cerebellum
   e.      The cerebellar vermis may be undetectable and there may be marked hydrocephalus
   3.       Which of the following is incorrect about lissencephaly?
   a.       Absence of sulci and convolutions in the cortex
   b.      Severe mental retardation, fits and decerebate rigidity are usual features
   c.       It is abnormal before  seven months of foetal life
   d.      It may occur spontaneously or inherited as autosomal recessive
   e.      Magnetic resonance imaging is useful in making the diagnosis
   4.       The following are disorders of neuronal migration in the brain during life in utero except:
   a.       Agyria
   b.      Pachygyria
   c.       Polymicrogyria
   d.      Heterotopic grey matter
   e.      None of the above
   5.       Usual indications for renal biopsy include the following except:
   a.       Nephrotic syndrome with serum hypocomplementaemia
   b.      Glomerulonephritis with evidence of streptococcal infection
   c.       Nephrotic syndrome in the first year of life
   d.      Steroid resistant nephrotic syndrome
   e.      Glomerulonephritis with absence of hypocomplementaemia
   6.       Prenatal diagnosis of sickle cell anaemia is made by:
   a.       Isoelectric focusing
   b.      Chorionic villous sampling
   c.       High performance liquid chromatography
   d.      Sickling test
   e.      Haemoglobin electrophoresis
   7.       Differential diagnosis of acute osteomyelitis include the following except:
   a.       Cellulitis
   b.      Ewing sarcoma
   c.       Scurvy
   d.      Acute leukaemia
   e.      None of the above
   8.       Which of the following is inconsistent with simple febrile convulsions?
   a.       Focal seizures
   b.      Normal electroencephalographic pattern
   c.       Seizure lasting less than 15 minutes
   d.      Not more than one episode of seizure in 24 hours
   e.      Absence of sequelae
   9.       Hyperparasitaemia in a child with malaria is defined as parasite density greater than............................per micro litre
   a.       100 000
   b.      150 000
   c.       200 000
   d.      250 000
   e.      300 000
   10.   Usual causes of heart failure in children include the following except:
   a.       Pneumonia
   b.      Hypoglycaemia
   c.       Severe malaria
   d.      Dehydration
   e.      Sickle cell disease
   
   
   ANSWERS
   Please click on the comment section below to reveal the answers.
   Have a great time here